Shone's syndrome: Insights from three-dimensional echocardiography

VIVAS, MARTÍN F.; POLITI, MARÍA T.; RIZNYK, LAURA M.; CASTRO, MARÍA F.; AVEGLIANO, GUSTAVO; RONDEROS, RICARDO

ECHOCARDIOGRAPHY (MOUNT KISCO, N.Y.)

WILEY-BLACKWELL PUBLISHING, INC

Año: 2018 vol. 35 p. 417 - 419

0742-2822

Shone´s syndrome is a rare congenital anomaly defined as the presence of at least two of the following heart obstructions: a mitral supravalvular ring, a ?parachute? mitral valve stenosis, subaortic stenosis, and aortic coarctation. A 58-year-old man presented with a mitral ring and a ?parachute? mitral valve on two-dimensional transthoracic echocardiography, raising suspicion of Shone´s syndrome. Three-dimensional transesophageal echocardiography revealed a subannular mitral ring inserted directly on the mitral leaflets, thus acting as a ?valvar ring.? This distinction can have therapeutic implications as a ?valvar? mitral ring could require valve repair or replacement, instead of simple resection.