INVESTIGADORES
ESPERANTE Sebastian Andres
artículos
PUJOLS, JORDI; FORNT-SUÑÉ, MARC; GIL-GARCÍA, MARCOS; BARTOLOMÉ-NAFRÍA, ANDREA; CANALS, FRANCESC; CEROFOLINI, LINDA; TEILUM, KAARE; BANCI, LUCIA; ESPERANTE, SEBASTIÁN A.; VENTURA, SALVADOR
MIA40 circumvents the folding constraints imposed by TRIAP1 function
JOURNAL OF BIOLOGICAL CHEMISTRY; Año: 2025 vol. 301
BORKOSKY, SILVIA S.; PERALTA-MARTINEZ, RAMON; ARMELLA-SIERRA, ALICIA; ESPERANTE, SEBASTIÁN A.; LIZÁRRAGA, LEONARDO; GARCÍA-PARDO, JAVIER; VENTURA, SALVADOR; SANCHEZ, IGNACIO E.; DE PRAT-GAY, GONZALO
EXPERIMENTAL KINETIC MECHANISM OF P53 CONDENSATION-AMYLOID AGGREGATION
BIOPHYSICAL JOURNAL; Año: 2025
ALICIA SIERRA; LOUREIRO MARIA EUGENIA; ESPERANTE SEBASTIÁN A; BORKOSKY SILVINA; GALLO GIOVANNA; DE PRAT GAY GONZALO; LOPEZ NORA
Nuclease Activity of the Junín Virus Nucleoprotein C-Terminal Domain
Viruses; Lugar: Nueva York; Año: 2023 vol. 15
SALGUEIRO MARIANO; CAMPOREALE GABRIELA; VISENTIN A; ARAN, MARTIN; PELLIZZA L; ESPERANTE SEBASTIAN; CORBAT A; GRECCO H; SOUSA B; ESPERÓN R; BORKOSKY, SILVINA S.; DE PRAT GAY, GONZALO
Molten Globule Driven and Self-downmodulated Phase Separation of a Viral Factory Scaffold: Phase separation of a viral replication scaffold
Journal of Molecular Biology; Lugar: nueva york; Año: 2023 vol. 435
ESPERANTE, S.A.; ALVAREZ-PAGGI, D.; SALGUEIRO, M.; DESIMONE, M.F.; DE OLIVEIRA, G.A.P.; ARÁN, M.; GARCÍA-PARDO, J.; APTEKMANN, A.A.; VENTURA, S.; ALONSO, L.G.; DE PRAT-GAY, G.
A finely tuned interplay between calcium binding, ionic strength and pH modulates conformational and oligomerization equilibria in the Respiratory Syncytial Virus Matrix (M) protein
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS; Año: 2022 vol. 731
ESPERANTE, SEBASTIÁN A.; VAREJAO, NATHALIA; PINHEIRO, FRANCISCA; SANT'ANNA, RICARDO; LUQUE-ORTEGA, JUAN ROMÁN; ALFONSO, CARLOS; SORA, VALENTINA; PAPALEO, ELENA; RIVAS, GERMÁN; REVERTER, DAVID; VENTURA, SALVADOR
Disease-associated mutations impacting BC-loop flexibility trigger long-range transthyretin tetramer destabilization and aggregation
JOURNAL OF BIOLOGICAL CHEMISTRY; Año: 2021 vol. 297 p. 1 - 14
CABALLERO, MAURICIO T; BIANCHI, ALEJANDRA M; GRIGAITES, SEBASTIAN DIAZ; DE LA IGLESIA NIVEYRO, PAOLA X; NUÑO, ALEJANDRA; VALLE, SANDRA; AFARIAN, GABRIELA; ESPERANTE, SEBASTIAN A; FERRETTI, ADRIAN J. P; JARES BAGLIVO, SOFIA; DE LUCA, JULIAN; ALVAREZ-PAGGI, DAMIAN; DIAMANTI, ADRIANA; BASSAT, QUIQUE; POLACK, FERNANDO P; ZEA, CRISTIAN M; CAPORAL, PAULA; RAKISLOVA, NATALIA; VARO, ROSAURO; HURTADO, JUAN CARLOS; DABBAH, MARCELO ISAAC; CARBALLO, ANA MARÍA; MADRID, LORENA; ARES, PATRICIA; HERNANDEZ, GABRIELA; BASANTA, LUCAS
Community Mortality Due to Respiratory Syncytial Virus in Argentina: Population-based Surveillance Study
CLINICAL INFECTIOUS DISEASES; Año: 2021 vol. 73 p. 210 - 217
LIBSTER, R.; MARC, G. PÉREZ; WAPPNER, D.; COVIELLO, S.; BIANCHI, A.; BRAEM, V.; ESTEBAN, I.; CABALLERO, M.T.; WOOD, C.; BERRUETA, M.; RONDAN, A.; LESCANO, G.; CRUZ, P.; RITOU, Y.; VIÑA, V. FERNÁNDEZ; PAGGI, D. ÁLVAREZ; ESPERANTE, S.; FERRETI, A.; OFMAN, G.; CIGANDA, Á.; RODRIGUEZ, R.; LANTOS, J.; VALENTINI, R.; ITCOVICI, N.; HINTZE, A.; OYARVIDE, M.L.; ETCHEGARAY, C.; NEIRA, A.; NAME, I.; ALFONSO, J.; CASTELO, R.; CARUSO, G.; RAPELIUS, S.; ALVEZ, F.; ETCHENIQUE, F.; DIMASE, F.; ALVAREZ, D.; ARANDA, S.S.; YANOTTI, C. SÁNCHEZ; DE LUCA, J.; BAGLIVO, S. JARES; LAUDANNO, S.; NOWOGRODZKI, F.; LARREA, R.; SILVEYRA, M.; LEBERZSTEIN, G.; DEBONIS, A.; MOLINOS, J.; GONZÁLEZ, M.; PEREZ, E.; KREPLAK, N.; ARGÜELLO, S. PASTOR; GIBBONS, L.; ALTHABE, F.; BERGEL, E.; POLACK, F.P.
Early high-titer plasma therapy to prevent severe Covid-19 in older adults
NEW ENGLAND JOURNAL OF MEDICINE; Año: 2021 vol. 384 p. 610 - 618
CABALLERO, MAURICIO T; GRIGAITES, SEBASTIAN DIAZ; DE LA IGLESIA NIVEYRO, PAOLA X; ESPERANTE, SEBASTIAN; BIANCHI, ALEJANDRA M; NUÑO, ALEJANDRA; VALLE, SANDRA; AFARIAN, GABRIELA; FERRETTI, ADRIAN J. P; BAGLIVO, SOFIA JARES; DE LUCA, JULIAN; ZEA, CRISTIAN M; CAPORAL, PAULA; LABANCA, MARIA JOSE; DIAMANTI, ADRIANA; ALVAREZ-PAGGI, DAMIAN; BASSAT, QUIQUE; POLACK, FERNANDO P; CARBALLO, ANA M; HERNANDEZ, GABRIELA; FIGUEROA, PAOLA; ARES, PATRICIA E; RODRIQUEZ PAQUETE, CESAR A
Uncovering Causes of Childhood Death Using the Minimally Invasive Autopsy at the Community Level in an Urban Vulnerable Setting of Argentina: A Population-Based Study
CLINICAL INFECTIOUS DISEASES; Año: 2021 vol. 73 p. 435 - 441
PINHEIRO, FRANCISCA; VAREJÃO, NATHALIA; ESPERANTE, SEBASTIAN; SANTOS, JAIME; VELÁZQUEZ?CAMPOY, ADRIÁN; REVERTER, DAVID; PALLARÈS, IRANTZU; VENTURA, SALVADOR
Tolcapone, a potent aggregation inhibitor for the treatment of familial leptomeningeal amyloidosis
FEBS JOURNAL; Año: 2020
CONCI, JULIETA; ALVAREZ-PAGGI, DAMIAN; DE OLIVEIRA, GUILHERME A. P.; PAGANI, TALITA D.; ESPERANTE, SEBASTIAN A.; BORKOSKY, SILVINA S.; ARAN, MARTIN; ALONSO, LEONARDO G.; MOHANA-BORGES, RONALDO; PRAT-GAY, GONZALO DE
Conformational Isomerization Involving Conserved Proline Residues Modulates Oligomerization of the NS1 Interferon Response Inhibitor from the Syncytial Respiratory Virus
BIOCHEMISTRY; Año: 2019 vol. 58 p. 2883 - 2892
WANG, WEIQIANG; NAVARRO, SUSANNA; AZIZYAN, RAFAYEL A.; BAÑO-POLO, MANUEL; ESPERANTE, SEBASTIAN A.; KAJAVA, ANDREY V.; VENTURA, SALVADOR
Prion soft amyloid core driven self-assembly of globular proteins into bioactive nanofibrils
Nanoscale; Año: 2019 vol. 11 p. 12680 - 12694
ALVAREZ PAGGI, D.; ESPERANTE, S.A.; SALGUEIRO, M.; CAMPOREALE, G.; OLIVEIRA, G.A.; PRAT GAY, G.
A conformational switch balances viral RNA accessibility and protection in a nucleocapsid ring model
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS; Año: 2019 vol. 671 p. 77 - 86
MOLINA, IVANA G.; ESPERANTE, SEBASTIAN A.; MARINO-BUSLJE, CRISTINA; CHEMES, LUCÍA B.; DE PRAT-GAY, GONZALO
Cooperative RNA Recognition by a Viral Transcription Antiterminator
JOURNAL OF MOLECULAR BIOLOGY; Año: 2018 vol. 430 p. 777 - 792
ESPERANTE, SEBASTIÁN A.; ALVAREZ-PAGGI, DAMIÁN; SALGUEIRO, MARIANO; DE PRAT GAY, GONZALO
Mechanism of Tetramer Dissociation, Unfolding, and Oligomer Assembly of Pneumovirus M2-1 Transcription Antiterminators
ACS Omega; Año: 2018 vol. 3 p. 14732 - 14745
MOLINA, IVANA G.; JOSTS, INOKENTIJS; ALMEIDA HERNANDEZ, YASSER; ESPERANTE, SEBASTIAN; SALGUEIRO, MARIANO; GARCIA ALAI, MARIA M.; DE PRAT-GAY, GONZALO; TIDOW, HENNING
Structure and stability of the Human respiratory syncytial virus M 2–1 RNA-binding core domain reveals a compact and cooperative folding unit
Acta Crystallographica Section F Structural Biology Communications; Año: 2017 vol. 74 p. 23 - 30
ESPERANTE, SEBASTIÁN A.; COVALEDA, GIOVANNI; TREJO, SEBASTIÁN A.; BRONSOMS, SÍLVIA; AVILES, FRANCESC X.; VENTURA, SALVADOR
Plasticity in the Oxidative Folding Pathway of the High Affinity Nerita Versicolor Carboxypeptidase Inhibitor (NvCI)
Scientific Reports; Lugar: Londres; Año: 2017 vol. 7
SANTANNA R; GALLEGO P; ROBINSON LZ; ALDA PEREIRA-HENRIQUES; NELSON FERREIA; FRANCISCA PINHEIRO; SEBASTIAN ESPERANTE; NURIA REIG; SALVADOR VENTURA
Repositioning tolcapone as a potent inhibitor of transthyretin amyloidogenesis and associated cellular toxicity.
NATURE COMMUNICATIONS; Año: 2016
NOVAL MG; ESPERANTE SA; MOLINA IG; CHEMES LUCIA
Intrinsic Disorder to Order Transitions in the Scaffold Phosphoprotein P from the Respiratory Syncytial Virus RNA Polymerase Complex.
BIOCHEMISTRY; Lugar: Washington; Año: 2016 vol. 55 p. 1441 - 1454
ESPERANTE SA, NOVAL MG, ALTIERI TA, DE OLIVEIRA GA, SILVA JL, DE PRAT-GAY G.
Fine modulation of the respiratory syncytial virus M2-1 protein quaternary structure by reversible zinc removal from its Cys(3)-His(1) motif.
BIOCHEMISTRY; Lugar: Washington; Año: 2013 vol. 52 p. 6779 - 6789
ESPERANTE SA, PARIS G, DE PRAT-GAY G.
Modular unfolding and dissociation of the human respiratory syncytial virus phosphoprotein p and its interaction with the m(2-1) antiterminator: a singular tetramer-tetramer interface arrangement.
BIOCHEMISTRY; Lugar: Washington; Año: 2012 vol. 51 p. 8100 - 8110
ESPERANTE SEBASTIÁN ANDRÉS; CHEMES LUCIA; SANCHEZ IGNACIO; DE PRAT GAY GONZALO
The respiratory syncytial virus transcription antiterminator M(2-1) is a highly stable, zinc binding tetramer with strong pH-dependent dissociation and a monomeric unfolding intermediate.
BIOCHEMISTRY; Lugar: Washington; Año: 2011 vol. 50 p. 8529 - 8539
TARGOVNIK HECTOR M, ESPERANTE SEBASTIAN A, RIVOLTA CARINA M
Genetics and phenomics of hypothyroidism and goiter due to thyroglobulin mutations.
MOLECULAR AND CELLULAR ENDOCRINOLOGY.; Lugar: Amsterdam; Año: 2010 vol. 322 p. 44 - 55
SEBASTIÁN A ESPERANTE, CARINA M. RIVOLTA, LUCRECIA MIRAVALLE, VIVIANA HERZOVICH, SONIA IORCANSKY, MARCO BARALLE, HÉCTOR M. TARGOVNIK
Identification and characterization of four PAX 8 rare sequence variants (p.T225R, p.L233L, p.G336S and p.A439A) in patients with congenital hypothyroidism and dysgenetic thyroid glands.
CLINICAL ENDOCRINOLOGY; Lugar: Oxford; Año: 2008 vol. 68 p. 828 - 835
SEBASTIAN A ESPERANTE, CARINA M RIVOLTA, MARIELA CAPUTO, ROGELIO GONZALEZ SARMIENTO, HECTOR MANUEL TARGOVNIK
Identification and characterization of new variants of three associated SNPs and a microsatellite in the TSH recpetor gene which are usefull for genetic studies.
Molecular and Cellular Probes; Lugar: England; Año: 2008 vol. 22 p. 281 - 286
CAPUTO M, RIVOLTA CM, ESPERANTE SA, GRUÑEIRO-PAPENDIECK L, CHIESA A, PELLIZAS CG, GONZÁLEZ-SARMIENTO R, TARGOVNIK HM
Congenital hypothyroidism with goitre caused by new mutations in the thyroglobulin gene.
CLINICAL ENDOCRINOLOGY; Lugar: Oxford. England; Año: 2007 vol. 67 p. 351 - 357
VIVIANA VARELA, CARINA M. RIVOLTA, SEBASTIÁN A. ESPERANTE, LAURA GRUÑEIRO-PAPENDIECK, ANA CHIESA AND HÉCTOR M. TARGOVNIK
Three Mutations (p.Q36H, p.G418fsX482, and g.IVS19-2A>C) in the Dual Oxidase 2 Gene Responsible for Congenital Goiter and Iodide Organification Defect
CLINICAL CHEMISTRY; Lugar: Washington. DC. USA; Año: 2006 vol. 52 p. 182 - 191
RIVOLTA CM, MOYA CM, ESPERANTE SA, GUTNISKY VJ, VARELA V, TARGOVNIK HM.
La tiroides como modelo de mecansimos moleculares en enfermedades genéticas
MEDICINA (BUENOS AIRES); Lugar: Buenos Aires; Año: 2005 vol. 65 p. 257 - 267
D BORELINA, S ESPERANTE, V GUTNISKY, V FERREIRO, M FERRER, F GILIBERTO, G FRECHTEL, L FRANCIPANE, I SZIJAN
Supernumerary marker 15 chromosome in a patient with Prader-Willi syndrome.
CLINICAL GENETICS; Lugar: Denmark; Año: 2004 vol. 65 p. 242 - 243
HECTOR M TARGOVNIK, CARINA M RIVOLTA, VIVIANA VARELA, SEBASTIAN A ESPERANTE, VIVIANA J GUTNISKY, SABINA DOMENE.
Aspectos Genéticos de las enfermedades tiroideas.
Bioquimica y Patologia Clinica.; Lugar: Buenos Aires; Año: 2004 vol. 68 p. 15 - 16
DANIEL BORELINA, NORA ENGEL, SEBASTIAN ESPERANTE, VERONICA FERREIRO, MARCELA FERRER, MARIA TORRADO, ERNESTO GOLDSCHMIDT, LILIANA FRANCIPANE AND IRENE SZIJAN
Combined Cytogenetic and Molecular Analyses for the Diagnosis of Prader-Willi/Angelman Syndromes
journal of biochemistry and molecular biology; Lugar: Seoul Korea; Año: 2004 vol. 37 p. 522 - 526
GILIBERTO F, FERREIRO V, DALAMÓN V, SURACE E, COTIGNOLA J, ESPERANTE S, BORELINA D, BARANZINI S, SZIJAN I.
Direct deletion analysis in two Duchenne muscular dystrophy symptomatic females using polymorphic dinucleotide (CA)n loci within the dystrophin gene.
Journal of Biochemistry and Molecular Biology; Lugar: Seoul Korea; Año: 2003 vol. 36 p. 179 - 184
RIVOLTA, CARINA; HERZOVICH, VIVIANA; ESPERANTE, SEBASTIÁN; LAZZATI, JUAN; IORCANSKY, SONIA; TARGOVNIK, HÉCTOR.
Identificación de una transición heterocigota 1012C>T (R338W) en el exón 9 del gen del receptor  de hormonas tiroideas en una familia con resistencia generalizada a hormonas tiroideas.
REVISTA ARGENTINA DE ENDOCRINOLOGIA Y METABOLISMO; Lugar: Buenos Aires, Argentina; Año: 2003 vol. 40 p. 165 - 171
RIVOLTA CM, ESPERANTE SA, GRUÑEIRO-PAPENDIECK L, CHIESA A, MOYA CM, DOMENÉ S, VARELA V, TARGOVNIK HM.
Five novel inactivating mutations in the thyroid peroxidase gene responsible for congenital goiter and iodide organification defect.
HUMAN MUTATION; Lugar: Hoboken, New Jersey; Año: 2003 vol. 22 p. 259 - 263
DALAMON V, SURACE E, BORELINA D, ZIEMBAR M, ESPERANTE S, FRANCIPANE L, DAVILA M, PARMA D, SZIJAN I.
Detection of mutations in argentine retinoblastoma patients by segregation of polymorphisms, exon analysis and cytogenetic test.
OPHTHALMIC RESEARCH.; Lugar: Uwe Pleyer, Berlin; Año: 2001 vol. 33 p. 336 - 339