INVESTIGADORES
POSADAS MARTINEZ Maria Lourdes
artículos
Título:
The Journey to Diagnosis of Light Chain Amyloidosis: A Real-World Experience from a Single Center in Latin America
Autor/es:
LUCRECIA LILIANA OSES; MARCELINA CARRETERO; MARIA LOURDES POSADAS MARTINEZ; ERIKA BARBARA BRULC; ELSA MERCEDES NUCIFORA; NATALIA PAOLA SCHUTZ
Revista:
BLOOD, THE JOURNAL OF THE AMERICAN SOCIETY OF HEMATOLOGY - ONLINE
Editorial:
Elsevier
Referencias:
Año: 2023
ISSN:
1528-0020
Resumen:
Light chain (AL) amyloidosis is a form of systemic amyloidosis, causing organ dysfunction; mainly affecting heart and kidneys. Due to the non-specific clinical manifestations, diagnosis is challenging and patients experience a long journey and treatment delay. Consequently, AL amyloidosis patients have extensive organ involvement at the time of diagnosis which implies a poor prognosis. Early diagnosis of AL amyloidosis is of paramount importance. There is limited real-world data from Latin America regarding the time from initial patient reported symptom onset to diagnosis.